Thursday 29 February 2024

Zinner Syndrome: A Comprehensive Case Report on Diagnosis and Management | Chapter 1 | Advancement and New Understanding in Medical Science Vol. 5

Zinner syndrome, a rare developmental anomaly of the urogenital tract, is a result of disrupted embryonic development of the genitourinary system. With approximately 100 reported cases, this condition is characterized by renal agenesis, ipsilateral seminal vesicle cyst, and vas deferens obstruction or dilation. Most patients remain asymptomatic, making early diagnosis challenging. Various radiologic modalities, including intravenous pyelography, ultrasonography, vasovesiculography, contrast-enhanced computed tomography (CT), and magnetic resonance imaging (MRI), contribute to accurate diagnosis. We present a case of Zinner syndrome, highlighting its rarity and the importance of vigilant imaging for identification. While asymptomatic patients necessitate active follow-up, those with symptomatic presentations may require surgical interventions, such as perineal cyst aspiration, subcutaneous cyst drainage, laparoscopic, or open surgery. Additionally, male patients should be monitored for potential infertility. Our case, involving a 17-year-old asymptomatic individual initially presenting with bilateral pneumonia, underscores the need for ongoing surveillance in managing Zinner syndrome.


Author(s) Details:

Vladimer Papava,
Department of Urology, Tbilisi State Medical University, Tbilisi, Georgia.

Tamar Didbaridze,
Tbilisi State Medical University, Tbilisi, Georgia.

Giorgi Sinauridze,
Department of Urology, Tbilisi State Medical University, Tbilisi, Georgia.

Magda Tsirekidze,
Department of Radiology, Tbilisi State Medical University, Tbilisi, Georgia.

Tamta Mamasakhlisi,
Department of Internal Medicine, Tbilisi State Medical University, Tbilisi, Georgia.

Valeriane Kvakhajelidze,
Department of Urology, Clinic ‘’Pineo’’, Tbilisi, Georgia.

Leli Shanidze,
Tbilisi State Medical University, Tbilisi, Georgia.

Zurabi Zaalishvili,
American Program of Tbilisi State Medical University, Tbilisi, Georgia.

Please see the link here: https://stm.bookpi.org/ANUMS-V5/article/view/13301

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