Splenogonadal fusion is an abnormal connection between the
spleen and gonads. This rare entity can be easily confused with testicular
tumors. It usually accompanies congenital malformations, such as
cryptorchidism, making diagnosis more difficult. Herein, we report two rare
cases of this challenging diagnosis. The first case involved a 5-year-old child
admitted for management of bilateral testicular cryptorchidism complicated by
an inguinal hernia on the left. Intraoperatively, we discover a globular left
testis with two red ovoid formations of 4mm. There was no connection between
the testis and the lower edge of the spleen. One of these formations was
biopsied, showing normal splenic parenchyma and confirming the diagnosis of
splenogonadal fusion. The second case was a 9-month-old infant followed for a
disorder of sex differentiation, stage III of Prader with a 46, XY genotype.
Diagnostic laparoscopy showed bilateral testicular cryptorchidism with
intraabdominal testes. There was a left testicular nodule connected to the
lower cryptorchidism edge of the spleen with a cord-like structure. A biopsy of
the nodule showed normal splenic parenchyma. Bilateral orchidopexy was
performed without removal of the left testicular nodule. Our two cases
highlight the fact that surgeons must be aware of this entity to avoid
unnecessary orchiectomy. In some cases, a biopsy may help with diagnosis.
Author(s) Details
Khouloud Ben Lazreg
Pathology Department, Habib Thameur Hospital, Tunis,
Tunisia.
Imen Helal
Pathology Department, Habib Thameur Hospital, Tunis, Tunisia
and Faculty of Medicine of Tunis, University
of Tunis El Manar, Tunis, Tunisia.
Fatma Khanchel
Pathology Department, Habib Thameur Hospital, Tunis, Tunisia
and Faculty of Medicine of Tunis, University of Tunis El Manar, Tunis, Tunisia.
Aida Daieb
Faculty of Medicine of Tunis, University of Tunis El Manar,
Tunis, Tunisia and Pediatric Surgery Department, Habib Thameur Hospital, Tunis,
Tunisia.
Sameh Tlili
Pediatric Surgery Department, Regional Hospital of Zaghouan,
Zaghouan, Tunisia.
Sirine El Fekih
Pathology Department, Habib Thameur Hospital, Tunis, Tunisia
and Faculty of Medicine of Tunis, University of Tunis El Manar, Tunis, Tunisia.
Ehsen Ben Brahim
Pathology Department, Habib Thameur Hospital, Tunis, Tunisia
and Faculty of Medicine of Tunis, University of Tunis El Manar, Tunis, Tunisia.
Youssef Hellal
Faculty of Medicine of Tunis, University of Tunis El Manar,
Tunis, Tunisia and Pediatric Surgery Department, Habib Thameur Hospital, Tunis,
Tunisia.
Raja Jouini
Pathology Department, Habib Thameur Hospital, Tunis, Tunisia
and Faculty of Medicine of Tunis, University of Tunis El Manar, Tunis, Tunisia.
Achraf Chadli
Debbiche
Pathology Department, Habib Thameur Hospital, Tunis, Tunisia
and Faculty of Medicine of Tunis, University of Tunis El Manar, Tunis, Tunisia.
Please see the link:- https://doi.org/10.9734/bpi/mria/v10/1124
No comments:
Post a Comment